An infant presented with a large soft tissue
mass-like lesion in the thigh. Reportedly the
previous surgical excision of the lesion had
revealed histopathological diagnosis of kaposiform hemangioendothelioma. Steroid
treatment was initiated; however, the patient
returned with clinical signs of hemorrhage.
Diagnostic work up revealed severe degree low
platelets, consistent with Kasabach
Merritt syndrome. Despite aggressive medical
therapy, the patient required angiographic
assessment, then transcatheter embolization. The
patient recovered completely.
hemangioendothelioma is associated with Kasabach
Merritt syndrome in some patients and may require
aggressive therapy. Although a surgical intervention
is needed in some patient, some benefit
significantly from transcatheter embolization. It is
important to follow these patients closely for potential
is an angiographic appearance of the lesion.
The lesion is quite hypervascular with
multiple small arterial feeders from iliac and
femoral arteries. It is impostant to note that
there are no arteriovenous shunts.