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Case#13 History:
Newborn with an obvious lesion in the thigh.
Etiology is unclear.
1st
photo is at birth and 2nd photo obtained a week
later.
Discussion:
This is a congenital lesion and the differential
should include congenital hemangioma (or rapidly
involuting congenital hemangioma - RICH) or
congenital sarcoma. Congenital sarcoma (fibrosarcoma)
is probably less common than RICH. Diagnosis of RICH
was made based on the lesion's appearance. Imaging
(typically MR or US) may be indicated to confirm the
diagnosis. Biopsy of the lesion may also be needed
in selected cases. Platelet count and thyroid hormone
levels needs to be checked. Imaging findings of this
condition may be quite confusing; probably this has
caused unnecessary interventions in many patients throughout
the country. If needed, transcatheter embolization
is the treatment of choice to close off some of the
arterial feeders, and surgery is required in small
number of patients. Medical management (drug
therapy) is similar to infantile hemangioma.
1st
photo obtained at 3 months and the 2nd photo
obtained at 5 months.
Diagnosis:
RICH
(Congenital hemangioma or Rapidly Involuting
Congenital hemangioma)
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