syndrome (Cutaneomeningospinal angiomatosis) consists
of a capillary malformation that has a high-flow
nature on the posterior thorax in association with a
spinal involvement (AVM
of the spine). Sometimes the vertebral bodies
are involved. Neurological problems commonly arise
due to cord compression or spinal hemorrhage. The
spinal AVMs are most commonly intramedullary, but
may be meningeal or perimedullary.
and/or conventional spinal arteriogram demonstrate a
high flow vascular anomaly.
rare occasions, the posterior AVM may be seen like a
port-wine stain (“pseudo-port-wine stain”).